It is caused when nerves become trapped in the wrist due to a lack of space which has been caused by inflammation and or scar tissue which has built up from repetitive trauma. Some neuropathies, like carpal tunnel, are quite common. Wartenberg s syndrome is a rare compression neuropathy of the sensory branch of the radial nerve and is characterized by pain and paresthesia in the radial dorsal forearm radiating to the back of the thumb and second and third fingers. Wartenberg symptom definition of wartenberg symptom by. A sensitive polyneuropathy without symptoms of motor loss, involving the superficial branch of the radial nerve, manifested by paraesthesia, dysaesthesia, or hyperaesthesia of the ulnar surface of the thumb. The indications for each type of treatment are discussed.
Wartenbergs syndrome is a specific mononeuropathy, caused by entrapment of the superficial branch of the radial nerve. Wartenberg neuritis is a pure sensory mononeuropathy characterized by sudden sensory loss and numbness of cutaneous nerves induced by stretch or trauma. Waardenburg syndrome ws is a group of genetic conditions characterized by varying degrees of hearing loss and differences in the coloring pigmentation of the eyes, hair, and skin. Since its original description in 1958 by wartenberg et al, 1 very few cases have been reported 2 12 supporting it being a rare disorder. Waardenburg syndrome type 2 ws2 is a type of waardenburg syndrome characterized by varying degrees of deafness and pigmentation coloring abnormalities of the eyes, hair andor skin. The superficial branch of the radial nerve has 3 or 4 terminal branches and is a purely sensory nerve as indicated by the shaded area. It was described in 1932 by wartenberg, who suggested the name cheiralgia paraesthetica. Isolated superficial radial neuropathy also called the wartenberg syndrome or cheiralgia paresthetica is a sensory mononeuropathy and a rare clinical. The topic wartenberg syndrome you are seeking is a synonym, or alternative name, or is closely related to the medical condition radial nerve dysfunction quick summary.
Les syndromes canalaires rares du membre superieur orbi. Signs and symptoms can vary both within and between families. Wartenbergs syndrome is a rare compression neuropathy of the sensory branch of the radial nerve and is characterized by pain and paresthesia in the radial dorsal forearm radiating to the back of the thumb and second and third fingers. In all patients the diagnosis was made on clinical grounds. Wartenberg syndrome also called isolated superficial radial neuropathy or cheiralgia paresthetica, is an entrapment neuropathy of the superficial branch of the radial nerve at the level of the distal forearm and wrist 1. The full text of this article is available in pdf format. Conservative treatment achieved 71% excellent and good results. The ulnar nerve begins at the side of the neck, travels behind the elbow and ends in the hand at the little and ring fingers. Waardenburg syndrome type 2 genetic and rare diseases. Guyons canal syndrome is a common nerve compression affecting the ulnar nerve as it passes through a tunnel in the wrist called guyons canal. The posterior interosseous nerve is a branch of the radial nerve, which. Educational video describing entrapment of the superficial radial nerve of the forearm. The etiology of the isolated superficial radial nerve neuropathy is often.
Eleven different waardenburg syndrome types have been described in the literature. Waardenburg syndrome is a term used to describe a collection of rare genetic conditions characterised by at least some degree of congenital hearing loss and pigmentation deficiencies, which can include bright blue eyes or one blue eye and one brown eye, a white forelock or patches of light skin. There have been many publications on this subject, even in recent years. Entrapment of the superficial branch of the radial nerve. There are multiple compression neuropathies of the upper extremity. Ws2 differs from type 1 and some other types of ws by the absence of dystopia canthorum lateral displacement of the inner canthi of the eyes. A positive tinelas sign over the course of the nerve is the most common physical examination finding. Wartenberg syndrome claim compensation wartenberg syndrome. Sometimes associated with cutaneous discoloration in the area of sensory. At the time, he suggested the name cheiralgia paraesthetica, because he observed a similarity to the isolated involvement of the thighs lateral cutaneous nerve.
The superficial branch of the radial nerve is highly vulnerable to trauma, irritation and compression due to its anatomical location. They frequently report symptom magnification with wrist movement or. Wartenberg syndrome, which is entrapment of the superficial ie, sensory branch of the radial nerve srn, was first described by dr. Cheiralgia paresthetica wartenbergs syndrome treatment. Common features include congenital sensorineural deafness. Patients with the diagnosis of wartenberg syndrome complain of pain over the distal radial forearm associated with paresthesias over the dorsal radial hand. Lateral antebrachial cutaneous nerve lacn neuritis. The case was presented because of disappearing his preoperative complaints after the operation with respect to wartenbergs syndrome.
Operation was followed by 74% excellent and good results. In group 1, conservative treatment of wartenbergs syndrome was used in 16 patients associated with surgical release of the first extensor. Cheiralgia, a term used for the fi rst time in describing wartenberg syndrome, is a neuropathy of the upper limb, underdiagnosed today, caused by compression or weft on the superfi cial branches of the radial nerve2,3. Although most people with waardenburg syndrome have normal hearing, moderate to profound hearing loss can occur in one or both ears. Symptoms include numbness, tingling, and weakness of the posterior aspect of the thumb. Compression can be idiopathic or traumatic due to direct compression, such as by handcuffs or tight watchbands, or due to distal radius fracture or. It can be secondary to tight watch band or handcuffs, compression from distal radius fracture or idiopathic. At the wrist, the ulnar nerve and artery run through the tunnel known as. The etiology of the isolated superficial radial nerve neuropathy is often associated with. Cheiralgia paresthetica wartenbergs syndrome treatment numbness or or tingling on the back of the wrist and hand can be a result of compression of the radial nerve between the tendons of the extensor carpi radialis longus and brachioradialis muscles. Nerve entrapment syndromes of the elbow, forearm, and. Waardenburg syndrome is a group of genetic conditions that can cause hearing loss and changes in coloring pigmentation of the hair, skin, and eyes. Intraneural lipoma of the radial nerve presenting as.
Attraversa il cavo ascellare portandosi nella regione posteriore del braccio dove emette rami motori per. The associated movement between the jaw and the upper eyelid described first by the london ophthalmologist marcus gunn in 1883 evoked great interest among neurologists and ophthalmologists. In this condition,the patient reports pain over the distal radial forearm associated with paresthesias over the dorsal radial hand. Lesions of the radial nerve at the level of the wrist are named wartenbergs syndrome. Intraneural lipomas and fibrolipomas arising from the supporting tissues of this peripheral nerve can cause compression of the adjacent nerve leading to symptoms of neuritis of the radial nerve or wartenberg syndrome. Wartenberg syndrome also known as cheiralgia paresthetica is due to compression of the superficial branch of the radial nerve in the distal forearm.
We have treated 50 patients 52 cases of entrapment of the sensory branch of the radial nerve in the forearm wartenberg syndrome between january 1988 and july 1992. Wartenberg syndrome, also called cheiralgia paresthetica, is compression of the superficial branch of the radial nerve, typically as the nerve assumes a superficial course in the distal forearm. Imaging can be used to evaluate a structural cause of the entrapment, such as a mass or enlarged muscle or to show secondary findings that confirm the diagnosis, such as nerve swelling or muscle edema or atrophy. Nerve entrapment syndromes usually have typical clinical presentations and findings on physical examination. Il nervo radiale prende origine dalle radici nervose c5c8t1. Wartenberg syndrome related to the use of splint during carpal. Hand surgery center, orthopedics department, italy. People with this condition often have very pale blue. Wartenberg s syndrome is described as the entrapment of the superficial branch of the radial nerve1 with only sensory manifestations and no motor deficits. Posterior interosseous nerve syndrome statpearls ncbi.
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